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Hemolytic Anemia as a Presenting Feature of Wilson’s Disease: A Case Report

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Indian Journal of Hematology and Blood Transfusion Aims and scope Submit manuscript

Abstract

Wilson’s disease is a rare inherited disorder of copper metabolism causing severe damage to vital organs. Liver and brain disorders are the main manifestations. Severe hemolytic anemia is an unusual complication of Wilson’s disease. We present a case who developed spherocytic acute hemolytic anemia (Coomb’s negative) as the initial manifestation of Wilson’s disease. On examination Kayser- Fleischer ring was found. Laboratory data supported a diagnosis of Wilson’s disease.

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Authors and Affiliations

  1. Department of Pathology, Lady Hardinge Medical College and Kalawati Saran Children’s Hospitals, New Delhi, 110001, India

    Sunita Sharma, Anupa Toppo, Aparna Harbhajanka & P. Lalita Jyotsna

  2. Department of Pediatrics, Lady Hardinge Medical College & Kalawati Saran Children’s Hospitals, New Delhi, 110001, India

    B. Rath

Authors
  1. Sunita Sharma
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  2. Anupa Toppo
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  3. B. Rath
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  4. Aparna Harbhajanka
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  5. P. Lalita Jyotsna
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Correspondence to Sunita Sharma.

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Sharma, S., Toppo, A., Rath, B. et al. Hemolytic Anemia as a Presenting Feature of Wilson’s Disease: A Case Report. Indian J Hematol Blood Transfus 26, 101–102 (2010). https://doi.org/10.1007/s12288-010-0034-2

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  • DOI: https://doi.org/10.1007/s12288-010-0034-2

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