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Familial hemophagocytic lymphohistiocytosis

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Indian Journal of Hematology and Blood Transfusion Aims and scope Submit manuscript

Abstract

A 45-day-old infant presented with hepatosplenomegaly and fever since 15 days. Hemogram revealed bicytopenia and bone marrow aspirate showed hemophagocytosis. With the history of death of two siblings, the baby was diagnosed with hemophagocytic lymphohistiocytosis (HLH), likely to be of familial origin.

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References

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Authors and Affiliations

  1. Department of Pathology, King Edward Memorial Hospital, Pune, India

    S. Raka, P. Nayar, R. Godbole & R. Manchanda

Authors
  1. S. Raka
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  2. P. Nayar
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  3. R. Godbole
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  4. R. Manchanda
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Corresponding author

Correspondence to R. Manchanda.

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Raka, S., Nayar, P., Godbole, R. et al. Familial hemophagocytic lymphohistiocytosis. Indian J Hematol Blood Transfus 25, 78–80 (2009). https://doi.org/10.1007/s12288-009-0018-2

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  • DOI: https://doi.org/10.1007/s12288-009-0018-2

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