Abstract
Desmoid tumors are uncommon, with an overall reported incidence of 2–5 per million population. They can be seen anywhere in the body. Desmoid tumors are associated with familial adenomatous polyposis especially with Gardner syndrome. In this study, we performed surgery for an abdominal mass involving the bladder, sigmoid colon, ileum, omentum, and rectus abdominis muscle macroscopically. A 50-year-old woman complained about abdominal distention of 1-year duration and abdominal pain for 2 months. In physical examination, tenderness was found at the lower quadrants of the abdomen and the suprapubic region. Computed tomography (CT) revealed a 43 × 43-mm mass lesion in the soft tissue densities. Magnetic resonance imaging (MRI) revealed a 43-mm lesion most likely a cyst or a sigmoid mass associated with sigmoid colon. Tumor was totally resected and pathologically diagnosed as fibromatosis. Differential diagnosis of the abdominal desmoid tumors could be difficult if the tumor is not settled in anterior preperitoneal space typically. Primary treatment of aggressive fibromatosis is surgery. Depending on the experience of the surgeon, recurrence rate varies between 25 and 65%. Radiotherapy is performed as adjuvant treatment for local control of the tumor or can be performed if the disease is extensive and local excision is not possible with surgery.
Similar content being viewed by others
References
Rizdwan A, Normala B (2008) Surgical management of large desmoid tumour of the anterior abdominal wall. Asian J surg 31(2):90–95
Mariani A, Nascimento AG, Webb MJ, Sim FH, Podratz KC (2000) Surgical management of desmoid tumors of female pelvis. J Am Coll Surg 191(2):175–183
Stoidis NC, Spyropoulos BG, Misiakos PE, Fountzilas CK, Paraskeva PP, Fotiadis CI (2010) Surgical treatment of giant mesenteric fibromatosis presenting as a gastrointestinal stromal tumor: a case report. J Med Case Rep 4:314
Kovačević K, Obad-Kovačević D, Popić-Ramač J (2017) Sporadic giant intra-abdominal desmoid tumor: a radiological case report. Mol Clin Oncol 6(6):896–898. https://doi.org/10.3892/mco.2017.1250
Kreuzberg B, Koudelova J, Ferda J, Treska V, Spitlen V, Mukensnabl P (2007) Diagnostic problems of abdominal desmoid tumors in various locations. Eur J Radiol 62:180–185
Kumar S, Singh SK, Acharya N, Naja V, Kamat R, Mandal AK Fibromatosis (desmoid tumor) in the urogenital system. Int J Gynecol Obstet 99(2):135–136
Oguz M, Bedirli A, Gültekin A, Dursun A, Menteş BB (2006) Desmoid tumor arising at the colostomy site after abdominoperineal resection for rectal carcinoma: report of a case. Dis Colon Rectum 49:1945–1948
Tolan A, Shanks JH, Loh MY, Taylor B, Wylie JP (2007) Fibromatosis: benign by name but not necessarily by nature. Clinical Oncology 19:319–326
Author information
Authors and Affiliations
Corresponding author
Ethics declarations
Conflict of Interest
The authors declare that they have no conflict of interest.
Additional information
Publisher’s Note
Springer Nature remains neutral with regard to jurisdictional claims in published maps and institutional affiliations.
Rights and permissions
About this article
Cite this article
Vural, V., Avanaz, A., Doğru, V. et al. Management of Abdominal Wall and Intraabdominal Fibromatosis with Multi-organ Involvement: a Case Report. Indian J Surg 82, 105–107 (2020). https://doi.org/10.1007/s12262-019-01932-1
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s12262-019-01932-1