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Persistent Müllerian Duct Syndrome: a Case Report

Indian Journal of Surgery volume 75, pages 460–462 (2013)Cite this article

Abstract

Persistent Müllerian duct syndrome is a rare form of internal male pseudohermaphroditism caused by defects in synthesis or action of Müllerian-inhibiting factor, due to which Müllerian duct derivatives, such as uterus, fallopian tube, and upper vagina, are normally present in 46XY males. Here, we report a 26-year-old male with right-sided obstructed inguinal hernia with left undescended testis. On exploration, hernial sac containing bowel loops, uterus with fallopian tubes, upper vagina, and testes were present.

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Affiliations

  1. Department of Surgery, B.L.D.E.U.’s Shri B.M. Patil Medical College & Research Centre, Bijapur, Karnataka, India

    Vijaya Patil

  2. Department of General Surgery, B.L.D.E.U.’s Shri B.M. Patil Medical College & Research Centre, Bijapur, Karnataka, India

    Sunilkrishna Muktinaini, Rashmi Patil & Ashish Verma

Authors
  1. Vijaya Patil
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  2. Sunilkrishna Muktinaini
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  3. Rashmi Patil
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  4. Ashish Verma
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Correspondence to Vijaya Patil.

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Patil, V., Muktinaini, S., Patil, R. et al. Persistent Müllerian Duct Syndrome: a Case Report. Indian J Surg 75, 460–462 (2013). https://doi.org/10.1007/s12262-013-0831-6

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  • DOI: https://doi.org/10.1007/s12262-013-0831-6

Keywords

  • Persistent Müllerian duct syndrome
  • Transverse testicular ectopia
  • Hernia uteri inguinale