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Malignant Triton Tumor: A Rare Case

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Abstract

Malignant triton tumor (MTT) is a malignant peripheral nerve sheath tumor (MPNST) with rhabdomyoblastic differentiation. This rare tumor, with fewer than 100 cases reported in the literature, generally affects adult patients with neurofibromatosis 1 (NF-1). We report such a case in a 34-year-old man with NF-1 who presented with a mass over the medial side of the arm. Histopathologically finding of rhabdomyoblasts among malignant Schwann cells in a tumor arising from a peripheral nerve supported by immunostaining with S-100 protein and myogenin confirmed the diagnosis. MTT has a poor prognosis owing to its aggressive biological behavior. The fact that this tumor is extremely rare has prompted us to report this case.

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Authors and Affiliations

  1. Department of Pathology and Surgical, Bhagwan Mahaveer Jain Hospital, Bangalore, Karnataka, 560052, India

    Prasad K. Shetty, Sameer V. Baliga & Kopparthi Balaiah

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  1. Prasad K. Shetty
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  2. Sameer V. Baliga
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  3. Kopparthi Balaiah
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Correspondence to Prasad K. Shetty.

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Shetty, P.K., Baliga, S.V. & Balaiah, K. Malignant Triton Tumor: A Rare Case. Indian J Surg 75 (Suppl 1), 362–365 (2013). https://doi.org/10.1007/s12262-012-0710-6

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  • DOI: https://doi.org/10.1007/s12262-012-0710-6

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