Abstract
We present a case of an 11-year-old boy, who presented to us with a ventral hernia since birth. He was found to have the following: A large ventral midline defect starting from umbilicus to xiphisternum. Sternum was bifid at the lower end. Liver had three separate lobes. Extrahepatic biliary apparatus was normal and liver was ptotic. Diaphragm had an anterior midline defect. Diaphragmatic defect was in continuity with pericardial defect and heart could be seen directly pulsating through the skin. Despite modern surgical standards, Cantrell’s syndrome represents a challenge to the surgeon because of the wide spectrum of anomalies, the severity of the abdominal and cardiac malformations, and the high mortality.
References
Cantrell JR, Haller JA, Ravitch MM (1958) A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium and heart. Surg Gynecol Obstet 107:602–614
Toyama WM (1972) Combined congenital defects of the anterior abdominal wall, sternum, diaphragm, pericardium, and heart a case report and review of the syndrome. Pediatrics 50:778–792
Jaime FV, Eberhard GM, Sabine D, Juergen K, Kyoichi N, Werner H, Bruno JM (1998) Cantrell’s syndrome: a challenge to the surgeon. Ann Thorac Surg 65:1178–1185
Welsh RJ, Ravitch MM (1986) Paediatric Surgery, 4th edn. Chicago, Vol 1. pp 566
Vanamo K, Sairanen H, Louhimo I (1991) The spectrum of Cantrell’s syndrome. Paediatr Surg Int 6:429–433
Fernandez MS, Lopez A, Vila JJ, Lluna J, Miranda J (1997) Cantrell’s pentalogy. Report of four cases and their management. Pediatr Surg Int 12(5–6):428–431
Okereke OUJ, Cooley DA, Frazier OH (1986) Congenital diverticulum of the ventricle. JTCVS 91:208–214
Zahka KG (1995) Associated abnormalities in children with congenital heart disease. In: Heart Disease in Infants, Children and Adolescents, 5th edn. Moss and Adams, Baltimore, Williams and Wilkins, pp 616
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Magadum, S., Shivaprasad, H., Dinesh, K. et al. Incomplete Cantrell’s Pentalogy—A Case Report. Indian J Surg 75 (Suppl 1), 350–352 (2013). https://doi.org/10.1007/s12262-012-0688-0
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s12262-012-0688-0