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Indian Journal of Surgery

, Volume 75, Supplement 1, pp 12–14 | Cite as

Retroperitoneal Peripheral Nerve Sheath Tumour of Triton Type—A Case Report

  • Dakshyani S. Nirhale
  • Amit Parasnis
  • Charit BoraEmail author
  • Ruchita Gupta
  • Prabhjot Aulakh
Case Report

Abstract

The malignant peripheral nerve sheath tumour is the malignant counterpart to benign soft tissue tumours such as neurofibromas and schwannomas. Malignant Triton Tumour is a histological variant of malignant peripheral nerve sheath tumours with rhabdomyosarcomatous differentiation. They are known to develop in cases of neurofibromatosis type 1 (von Recklinghausen’s disease). Malignant peripheral nerve sheath tumor is biologically an aggressive tumour for which the treatment of choice is surgery. Here we report a rare case of malignant peripheral nerve sheath tumour, not associated with neurofibromatosis type 1 and arising in the retroperitoneum.

Keywords

Peripheral nerve sheath tumour Malignant triton tumour Neurofibromatosis 

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Copyright information

© Association of Surgeons of India 2011

Authors and Affiliations

  • Dakshyani S. Nirhale
    • 1
  • Amit Parasnis
    • 1
  • Charit Bora
    • 1
    Email author
  • Ruchita Gupta
    • 1
  • Prabhjot Aulakh
    • 1
  1. 1.Department of General SurgeryPadmashree Dr. D. Y. Patil Medical Hospital and Research CentrePimpriIndia

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