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Loss of vision associated with angioid streaks in β-thalassemia intermedia

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Abstract

An acquired diffuse elastic tissue defect that resembles inherited pseudoxanthoma elasticum (PXE) has been noticed with a significant age-related frequency in hemoglobin disorders, especially β-thalassemia and has been held responsible for a number of complications observed in these cases, some of which are quite severe. We report here two patients with β-thalassemia intermedia, who presented with severe visual acuity impairment associated with angioid streaks, the typical ocular manifestation of PXE.

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Authors and Affiliations

  1. First Department of Internal Medicine, University of Athens Medical School, “Laiko” General Hospital, 17 Aghiou Thoma St, 115 27, Athens, Greece

    Athanasios Aessopos, Charalampos S. Floudas, Maria Kati, Maria Tsironi, Xanthoula Giakoumi, Charalampos Livir-Rallatos & Dimitrios Farmakis

  2. 50, Alexandroupoleos St, 115 27, Athens, Greece

    Charalampos S. Floudas

Authors
  1. Athanasios Aessopos
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  2. Charalampos S. Floudas
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  3. Maria Kati
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  4. Maria Tsironi
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  5. Xanthoula Giakoumi
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  6. Charalampos Livir-Rallatos
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  7. Dimitrios Farmakis
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Corresponding author

Correspondence to Charalampos S. Floudas.

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Aessopos, A., Floudas, C.S., Kati, M. et al. Loss of vision associated with angioid streaks in β-thalassemia intermedia. Int J Hematol 87, 35–38 (2008). https://doi.org/10.1007/s12185-007-0014-y

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  • DOI: https://doi.org/10.1007/s12185-007-0014-y

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