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Regional Odontodysplasia Affecting the Maxilla

  • Sine qua non Radiology-Pathology
  • Published:
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Abstract

Regional odontodysplasia (RO) is a rare dental anomaly of unknown etiology that can affect both deciduous and permanent dentition. RO is characterized by severe hypoplasia of enamel and dentin, and teeth affected are friable and more susceptible to caries and fractures. Most of the lesions occur in the anterior maxilla and correlation with clinical and radiographic features is essential to provide a correct diagnosis. The major criteria for diagnosis are predominantly based on radiography, which shows presence of large pulp chambers and a marked reduction in the radiopacity of enamel and dentin, making the distinction between these mineralized structures difficult. Early diagnosis is important to minimize future sequels and allow preventive or conservative treatment. The therapeutic approach of the RO should be based on the degree of severity of the anomaly and in the individual functional and aesthetic needs of each case. A classic case of RO affecting the maxilla is exemplified in this Sine Qua Non Radiology–Pathology article.

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Authors and Affiliations

  1. Laboratory of Morphology and Experimental Pathology, Institute of Technology and Research, Tiradentes University (UNIT), Avenida Murilo Dantas, 300, Aracaju, SE, 49032-490, Brazil

    John Lennon Silva Cunha & Ricardo Luiz Cavalcanti de Albuquerque-Júnior

  2. Department of Dentistry, Federal University of Sergipe (UFS), Aracaju, SE, Brazil

    Albert Vinicius Barboza Santana, Lucas Alves da Mota Santana, Daniela Meneses Santos & Liane Maciel de Almeida Souza

  3. Department of Physiological Sciences, Piracicaba Dental School, University of Campinas (UNICAMP), Piracicaba, SP, Brazil

    Klinger de Souza Amorim

  4. Department of Oral Surgery and Pathology, School of Dentistry, Universidade Federal de Minas Gerais, Belo Horizonte, MG, Brazil

    Sílvia Ferreira de Sousa

Authors
  1. John Lennon Silva Cunha
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  2. Albert Vinicius Barboza Santana
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  3. Lucas Alves da Mota Santana
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  4. Daniela Meneses Santos
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  5. Klinger de Souza Amorim
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  6. Liane Maciel de Almeida Souza
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  7. Sílvia Ferreira de Sousa
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  8. Ricardo Luiz Cavalcanti de Albuquerque-Júnior
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Correspondence to John Lennon Silva Cunha.

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No identifier information is included in the case report, and the study meets the waiver criteria for the institutional review board of Tiradentes University.

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Silva Cunha, J.L., Barboza Santana, A.V., Alves da Mota Santana, L. et al. Regional Odontodysplasia Affecting the Maxilla. Head and Neck Pathol 14, 224–229 (2020). https://doi.org/10.1007/s12105-019-01031-3

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  • DOI: https://doi.org/10.1007/s12105-019-01031-3

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