The Indian Journal of Pediatrics

, Volume 86, Issue 9, pp 857–859 | Cite as

Fatal Myocarditis in an Adolescent Girl with Evolving Connective Tissue Disease

  • Bipin JoseEmail author
  • Dantis Emmanuel
  • Preethy Harrison
Clinical Brief


Connective tissue diseases are rarely suspected and diagnosed in childhood and adolescence. Rarity of occurrence and poor disease acceptance among parents make them extremely difficult to treat in the early stages. An adolescent girl presented with features of pneumonia, was worked up and diagnosed as an evolving connective tissue disease. Her clinical characteristics did not fit into any specific disease. She was started on steroids and immunoglobulin as she had fulminant myocarditis with rapid downhill clinical course. High index of suspicion and aggressive immunosuppression can be life saving in exceptional situations even though a specific diagnosis cannot be ascertained.


Myocarditis Connective tissue disease Children Gottron’s papules Raynaud’s 


Authors’ Contribution

BJ: Involved in patient care, review of literature and drafting the manuscript; DE and PH: Involved in patient care, critical review and drafting the manuscript. Dr. Maj Gen (Retd) MNG Nair, Senior Consultant and Lead Pediatrics, Rajagiri Hospital, Aluva, Kerala will act as guarantor for this paper.

Compliance with Ethical Standards

Conflict of Interest



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Copyright information

© Dr. K C Chaudhuri Foundation 2019

Authors and Affiliations

  1. 1.Department of PediatricsRajagiri HospitalAluvaIndia
  2. 2.Department of Clinical Immunology and RheumatologyRajagiri HospitalAluvaIndia
  3. 3.Department of DermatologyRajagiri HospitalAluvaIndia

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