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Hirschsprung Disease — Current Diagnosis and Management

Abstract

Hirschsprung disease is a common cause of neonatal and infantile large gut obstruction. It is characterised by varying extent of contiguous aganglionosis extending from the anorectum proximally. Since its recognition, the diagnosis and management has continuously evolved with advances in histological evaluation and surgical techniques. This article summarizes the current modalities of investigation and optimal surgical management of Hirschsprung disease and concludes with a reference to the Indian scenario.

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Acknowledgements

The authors acknowledge the contribution of several faculty members from the Departments of Pediatric Surgery and Pathology**, St. John’s Medical College Hospital, Bangalore who have been part of the ‘Hirschsprung Team’ at the Academy from 1998 to 2017: Ashley D’Cruz, Usha Kini**, M K Babu**, Anand Alladi, Sanjay Rao, Antony Robert Charles, Mainak Deb, Shubha AM, Divya P**, Nandeesh BN**, Saleem KM, Prasanna Kumar AR, Kiran M, Lokendra Yadav**, Maria Bukelo** & Amanda Pinto**.

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KD and SM have jointly prepared the manuscript and are responsible for the intellectual content. KD will act as guarantor for the paper.

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Correspondence to Kanishka Das.

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Das, K., Mohanty, S. Hirschsprung Disease — Current Diagnosis and Management. Indian J Pediatr 84, 618–623 (2017). https://doi.org/10.1007/s12098-017-2371-8

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  • DOI: https://doi.org/10.1007/s12098-017-2371-8

Keywords

  • Hirschsprung disease
  • Current diagnosis
  • Management
  • Indian