The Indian Journal of Pediatrics

, Volume 84, Issue 8, pp 618–623 | Cite as

Hirschsprung Disease — Current Diagnosis and Management

Review Article


Hirschsprung disease is a common cause of neonatal and infantile large gut obstruction. It is characterised by varying extent of contiguous aganglionosis extending from the anorectum proximally. Since its recognition, the diagnosis and management has continuously evolved with advances in histological evaluation and surgical techniques. This article summarizes the current modalities of investigation and optimal surgical management of Hirschsprung disease and concludes with a reference to the Indian scenario.


Hirschsprung disease Current diagnosis Management Indian 



The authors acknowledge the contribution of several faculty members from the Departments of Pediatric Surgery and Pathology**, St. John’s Medical College Hospital, Bangalore who have been part of the ‘Hirschsprung Team’ at the Academy from 1998 to 2017: Ashley D’Cruz, Usha Kini**, M K Babu**, Anand Alladi, Sanjay Rao, Antony Robert Charles, Mainak Deb, Shubha AM, Divya P**, Nandeesh BN**, Saleem KM, Prasanna Kumar AR, Kiran M, Lokendra Yadav**, Maria Bukelo** & Amanda Pinto**.


KD and SM have jointly prepared the manuscript and are responsible for the intellectual content. KD will act as guarantor for the paper.

Compliance with Ethical Standards

Conflict of Interest


Source of Funding



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Copyright information

© Dr. K C Chaudhuri Foundation 2017

Authors and Affiliations

  1. 1.Department of Pediatric SurgerySt. John’s Medical College & HospitalBangaloreIndia
  2. 2.Department of PathologySt. John’s Medical CollegeBangaloreIndia

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