The Indian Journal of Pediatrics

, Volume 80, Issue 11, pp 968–971 | Cite as

Incontinentia Pigmenti Presenting as Encephalopathy

  • Vykuntaraju K. N. Gowda
  • Chandra Mouly
  • Asthik Biswas
  • Shivananda Shivananda
Clinical Brief


Incontinentia Pigmenti is a rare neurocutaneous disorder that may present with neurological symptoms in early infancy in addition to characteristic skin rashes. We report a two-mo-old girl presenting with a rash and encephalopathy. Magnetic resonance imaging of brain showed hemorrhagic infarcts. First we thought baby was suffering from a skin infection with meningo-encephalitis and later with development of characteristic skin lesions, neuroimaging and skin biopsy changes we reconsidered our diagnosis as Incontinentia pigmenti.


Incontinentia pigmenti Encephalopathy Skin rashes Seizures 


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Copyright information

© Dr. K C Chaudhuri Foundation 2012

Authors and Affiliations

  • Vykuntaraju K. N. Gowda
    • 1
  • Chandra Mouly
    • 1
  • Asthik Biswas
    • 1
  • Shivananda Shivananda
    • 1
  1. 1.Indira Gandhi Institute of Child HealthBangaloreIndia

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