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Total Colonic Aganglionosis—A Diagnostic Intricacy

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Abstract

Total colonic aganglionosis (TCA) is an unusual variety of aganglionosis. Although appearing to be an extension of Hirschprung’s disease (HD), it may differ from it in many ways and thus is difficult to diagnose on the basis of features applied for HD. The aim of this case report is to discuss the difficulties encountered in recognition of TCA and identification of features which can help in early diagnosis.

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Contributions

SC: acquisition of data, literature review and draft of the article; SN: main concept, will act as guarantor; AS: revised and gave final approval.

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Authors and Affiliations

  1. Department of Pediatrics and Neonatology, Lady Harding Medical College and Associated Kalawati Saran Children’s Hospital, New Delhi, India

    Sudha Chandelia, Sushma Nangia & Arvind Saili

  2. 28, Tekhand, Okhla Industrial Area, Phase-1, New Delhi, 110020, India

    Sudha Chandelia

Authors
  1. Sudha Chandelia
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  2. Sushma Nangia
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  3. Arvind Saili
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Correspondence to Sudha Chandelia.

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Chandelia, S., Nangia, S. & Saili, A. Total Colonic Aganglionosis—A Diagnostic Intricacy. Indian J Pediatr 80, 789–790 (2013). https://doi.org/10.1007/s12098-012-0822-9

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  • DOI: https://doi.org/10.1007/s12098-012-0822-9

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