Skip to main content
Log in

Caroli’s syndrome with ureterovesical calculi in a young child

  • Clinical Brief
  • Published:
The Indian Journal of Pediatrics Aims and scope Submit manuscript

Abstract

An 18-month-old boy was admitted with fever, abdominal pain, and hepatomegaly. CT scan revealed dilatation of intrahepatic biliary radicals with central dot sign, bilateral nephrocalcinosis, multiple ureteric and urinary bladder stones and right-sided obstructive hydroureteronephrosis due to a ureterovesical calculus of about 1.5 cm. Liver biopsy showed early hepatic fibrosis.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Similar content being viewed by others

References

  1. Yonem O, Bayraktar Y. Clinical characteristics of Caroli’s syndrome. World J Gastroenterol 2007; 13: 1934–1937.

    PubMed  Google Scholar 

  2. Bismuth H, Krissat J. Choledochal cystic malignancies. Ann Oncol 1999; 10: 94–99.

    Article  PubMed  Google Scholar 

  3. Miller WJ, Sechtin AG, Campbell WL, Pieters PC. Imaging findings in Caroli’s disease. Am J Roentgenol 1995; 165: 333–337.

    CAS  Google Scholar 

  4. Jonas MM, Perez-Atayde AR. Fibrocystic liver disease. In Suchy FJ, Sokol RJ, Balistreri WF, eds. Liver Disease in Children, 2nd ed. Philadelphia; Lippincott Williams & Wilkins; 2001; 904–905.

    Google Scholar 

  5. Lu SC, Debian KA. Cystic diseases of the biliary tract. In Yamada T, Alpers DH, Kaplowitz N, Laine L, Owyang C, Powell DW, eds. Textbook of Gastroenterology. Philadelphia; Lippincott Williams and Wilkins, 2003; 2225–2233.

    Google Scholar 

  6. Lavy AD, Charles A, Rohrmann JR, Linda A Murakat, Gael J Lonergan. Caroli disease. Radiological spectrum with pathologic correlation. Am J Roentgenol 2002; 179: 1053–1057.

    Google Scholar 

  7. Miller WJ, Sechtin AG, Campbell WL, Pecters PC. Imaging findings in caroli disease. Am J Roentgenol 1995; 165: 333–337.

    CAS  Google Scholar 

  8. Li J, Qiu ZQ, Wei M. Caroli’s syndrome. Zhongguo Dang Dai Er Ke Za Zhi 2009; 11: 10–14.

    PubMed  Google Scholar 

  9. Espinosa Aguilar E, López de Hierro Ruiz M, Pinel Julián LM, González Galilea A, Suárez Crespo JF, Ruiz-Cabello M. Caroli’s syndrome: a variable entity. Rev Esp Enferm Dig 1994; 86: 849–852.

    CAS  PubMed  Google Scholar 

  10. Mrowka C, Adam G, Sieberth HG, Matern S. Caroli’s syndrome associated with medullary sponge kidney and Nephrocalcinosis. Nephrol Dial Transplant 1996; 11: 1142–1145.

    CAS  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Tanu Midha.

Rights and permissions

Reprints and permissions

About this article

Cite this article

Rao, Y.K., Midha, T. Caroli’s syndrome with ureterovesical calculi in a young child. Indian J Pediatr 77, 701–702 (2010). https://doi.org/10.1007/s12098-010-0084-3

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s12098-010-0084-3

Key words

Navigation