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Diagnosis and management of cyanotic congenital heart disease: Part I

The Indian Journal of Pediatrics volume 76, pages 57–70 (2009)Cite this article

Abstract

Most commonly encountered cyanotic cardiac lesions in children, namely, tetralogy of Fallot, transposition of the great arteries and tricuspid atresia are reviewed. Pathology, pathophysiology, clinical features, non-invasive and invasive laboratory studies and management are discussed. The clinical and non-invasive laboratory features are sufficiently characteristic for making the diagnosis and invasive cardiac catheterization and angiographic studies are not routinely required and are needed either to define features, not clearly defined by non-invasive studies or as a part of catheter-based intervention. Surgical correction or effective palliation can be undertaken with relatively low risk. However, residual defects, some requiring repeat catheter or surgical intervention, are present in a significant percentage of patients and therefore, continued follow-up after surgery is mandatory.

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References

  1. Rao PS. Diagnosis and management of acyanotic heart disease: Part I — obstructive lesions. Indian J Pediatr 2005; 72: 496–502.

    Google Scholar 

  2. Rao PS. Diagnosis and management of acyanotic heart disease: Part II — left-to-right shunt lesions. Indian J Pediatr 2005; 72: 503–512.

    Article  Google Scholar 

  3. Fyler DC, ed. Nadas’ Pediatric Cardiology. Philadelphia, PA, Hanley & Belfus, Inc., 1992.

    Google Scholar 

  4. Rao PS. Pathophysiologic consequences of cyanotic heart disease. Indian J Pediat 1983; 50: 479–487.

    Article  CAS  PubMed  Google Scholar 

  5. Guntheroth WG, Morgan BC, Mullin GL. Physiologic studies of paroxysmal hyperpnea in cyanotic congenital heart disease. Circulation 1965; 31: 70–76.

    CAS  PubMed  Google Scholar 

  6. Rao PS. Congenital heart disease. In Rakel RE ed. Conn’s Current Therapy, Philadelphia, PA; W.B. Saunders. 1989; 2010–2013.

    Google Scholar 

  7. Rao PS, Brais M. Balloon pulmonary valvuloplasty for congenital cyanotic heart defects. Am Heart J 1988; 115: 1105–1110.

    Article  CAS  PubMed  Google Scholar 

  8. Rao PS, Wilson AD, Thapar MK, Brais M. Balloon pulmonary valvuloplasty in the management of cyanotic congenital heart defects. Cathet Cardiovasc Diagn 1992; 25: 16–24.

    Article  CAS  PubMed  Google Scholar 

  9. Rao PS. Transcatheter management of cyanotic congenital heart defects: a review. Clin Cardiol 1992; 15: 483–496.

    Article  CAS  PubMed  Google Scholar 

  10. Rao PS. Pulmonary valve in cyanotic heart defects with pulmonary oligemia. In Sievert H, Qureshi SA, Wilson N, Hijazi Z eds. Percutaneous Interventions in Congenital Heart Disease, Informa Health Care; Oxford, UK, 2007; 197–200.

    Google Scholar 

  11. Blalock A, Taussig HB. The surgical treatment of malformations of the heart in which there is pulmonary stenosis or pulmonary atresia. J Am Med Assoc 1945; 128:189–194.

    Google Scholar 

  12. de Leval MR, McKay R, Jones M Modified Blalock-Taussig shunt. Use of subclavian artery orifice as flow regulator in prosthetic systemic-pulmonary artery shunts. J Thorac Cardiovasc Surg 1981; 81: 112–119.

    PubMed  Google Scholar 

  13. Rashkind WJ, Miller WW. Creation of an atrial septal defect without thoracotomy. J Am Med Assoc 1966; 196: 991–992.

    Article  CAS  Google Scholar 

  14. Rao PS. Role of Interventional Cardiology In Neonates: Part I. Non-Surgical Atrial Septostomy. Neonatology Today 2007; 2: 9–14.

    Google Scholar 

  15. Jatene AD, Fontes VF, Paulista PP et al. Anatomic correction of transposition of the great vessels. J Thorac Cardiovasc Surg 1976; 72: 364–370.

    CAS  PubMed  Google Scholar 

  16. Rao PS. Tricuspid Atresia. NY; Mt Kisco, Futura Publishing Co, 1982.

    Google Scholar 

  17. Rao PS: Tricuspid atresia. In: Long WA, ed. Fetal and Neonatal Cardiology. Philadelphia; WB Saunders Co, 1990; 525–540.

    Google Scholar 

  18. Rao PS. Tricuspid Atresia. Mt Kisco, NY: Futura Publishing Co; 1992.

    Google Scholar 

  19. Rao PS. Tricuspid Atresia. In Pediatric Cardiovascular Medicine. Moller JH, Hoffman JIE eds. New York, NY Churchill Livingstone, 2000; 421–441.

    Google Scholar 

  20. Rao PS. Tricuspid Atresia. In e-medicine — Pediatrics http://www.emedicine.com

  21. Rao PS. A unified classification for tricuspid atresia. Am Heart J 1980; 99: 799–804.

    Article  CAS  PubMed  Google Scholar 

  22. Rudolph AM. Congenital Disease of the Heart. Year-Book Medical Publishers, Inc., Chicago, IL, 1974.

    Google Scholar 

  23. Rao PS. Cardiac catheterization in tricuspid atresia. In: Rao PS, ed. Tricuspid Atresia. 2nd ed. Mt Kisco, NY: Futura Publishing Co; 1992; 153–178.

    Google Scholar 

  24. Fontan F, Baudet E: Surgical repair of tricuspid atresia. Thorax 1971; 26: 240–248.

    Article  CAS  PubMed  Google Scholar 

  25. Kreutzer G, Bono H, Galindez E et al. Una operacion para la correccion de la atresia tricuspidea. Ninth Argentinean Congress of Cardiology, Buenos Aires, Argentina, Oct. 31–Nov. 6, 1971.

  26. Rao PS. Natural history of the ventricular septal defect in tricuspid atresia and its surgical implications. Br Heart J 1977; 39: 276–288.

    Article  CAS  PubMed  Google Scholar 

  27. Rao PS. Further observations on the spontaneous closure of physiologically advantageous ventricular septal defects in tricuspid atresia: surgical implications. Ann Thorac Surg 1983; 35: 121–131.

    Article  CAS  PubMed  Google Scholar 

  28. Bonnet D, Sidi D, Vouhe PR. Absorbable pulmonary artery banding in tricuspid atresia. Ann Thorac Surg 2001; 71: 360–361.

    Article  CAS  PubMed  Google Scholar 

  29. Rao PS. Absorbable pulmonary artery band in tricuspid atresia (editorial). Ann Thorac Surg 2001; 71: 361–362.

    Article  Google Scholar 

  30. deLeval MR, Kilner P, Gewilling M et al. Total cavopulmonary connection: a logical alternative to atriopulmonary connection for complex Fontan operation. J Thorac Cardiovasc Surg 1988; 96: 682–695.

    CAS  Google Scholar 

  31. Konertz W, Schneider M, Herwig V et al. Modified hemi-Fontan operation and subsequent nonsurgical Fontan completion. J Thorac Cardiovasc Surg 1995; 110: 865–867.

    Article  CAS  PubMed  Google Scholar 

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Authors and Affiliations

  1. Division of Pediatric Cardiology, Department of Pediatrics University of Texas-Houston Medical School/Children’s Memorial Hermann Hospital, Houston, Texas, USA

    P. Syamasundar Rao

  2. Division of Pediatric Cardiology, UT-Houston Medical School, 6431 Fannin, MSB 3.132, Houston, TX, 77030, USA

    P. Syamasundar Rao

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  1. P. Syamasundar Rao
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Correspondence to P. Syamasundar Rao.

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Rao, P.S. Diagnosis and management of cyanotic congenital heart disease: Part I. Indian J Pediatr 76, 57–70 (2009). https://doi.org/10.1007/s12098-009-0030-4

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  • DOI: https://doi.org/10.1007/s12098-009-0030-4

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