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Reactive Hemophagocytic syndrome

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Abstract

We describe two cases of Reactive Hemophagocytic syndrome (RHS) occurring in rheumatic diseases in childhood. Patient 1, an adolescent girl with systemic onset Juvenile idopathic arthritis (JRA) presented like severe sepsis with shock, hepatic dysfunction and coagulopathy. Patient 2 presented with cardiac tamponade, she was later detected to have systemic lupus erythematosus (SLE). Her bone marrow aspirate revealed prominent hemophagocytosis. Both cases improved with pulse methylprednisolone therapy.

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Authors and Affiliations

  1. Department of Pediatrics, Amrita Institute of Medical Sciences and Research Center, Kochi, Kerala, India

    L. Rajam, Vinitha Prasad & B.L. Yatheesha

  2. Amrita Institute of Medical Sciences and Research Centre, Elamakkara (P.O), Kochi, Kerala, 682026, India

    Vinitha Prasad

Authors
  1. L. Rajam
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  2. Vinitha Prasad
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  3. B.L. Yatheesha
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Correspondence to Vinitha Prasad.

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Rajam, L., Prasad, V. & Yatheesha, B. Reactive Hemophagocytic syndrome. Indian J Pediatr 75, 1261–1263 (2008). https://doi.org/10.1007/s12098-008-0170-y

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  • DOI: https://doi.org/10.1007/s12098-008-0170-y

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