Abstract
Caroli disease is a rare congenital malformation characterized by cystic dilatations of large bile ducts. There are two forms of Caroli disease. Simple form entails the bile duct dilatation or ectasia. Complex form is copresence of hepatic fibrosis and portal hypertension. Here is presented a case of central diabetes insipidus (CDI) associated with Caroli disease.
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References
Summerfield JA, Nagafuchi Y, Sherlock S et al. Hepatobiliary fibropolycystic diseases. A clinical and histological review of 51 patients. J Hepatol 1986; 2: 141.
Desmet VJ. Congenital diseases of intrahepatic bile ducts: variations on the theme “ductal plate malformation”. Hepatology 1992; 16: 1069.
Desmet VJ. What is congenital hepatic fibrosis?. Histopathology 1992; 20: 465.
Ward CJ, Hogan MC, Rossetti S et al. The gene mutated in autosomal recessive polycystic kidney disease encodes a large, receptor-like protein. Nat Genet 2002; 30: 259.
Squires RH, Weinberg AG, Zwiener RJ, Winick N. Langerhans’ cell histiocytosis presenting with hepatic dysfunction. J Paediatr Gastroenterol Nutr 1993; 16: 190–193.
Charach G, Sztern M, Yosipov Y, Blum I. Central diabetes insipidus as presenting sign of metastatic clear cell carcinoma. Isr J Med Sci 1990; 26: 580–582.
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Cetinkaya, S. Central diabetes insipidus associated with Caroli syndrome. Indian J Pediatr 74, 419–420 (2007). https://doi.org/10.1007/s12098-007-0072-4
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DOI: https://doi.org/10.1007/s12098-007-0072-4