Dermatofibrosarcoma Protuberans of the Neck: A Brief Review of the Literature

  • Sevim Aslan Felek
  • Mustafa İbas
  • Songul Dursun
  • Aylin Okcu Heper
Clinical Report


Dermatofibrosarcome protuberance (DFSP) is a rare, slow growing soft tissue sarcoma with fibroblastic origin, which has a great, potential of local invasion and recurrence. Because of its unspecific appearance and slow growth features it is commonly misdiagnosed as other benign lesions that leads to a late accurate diagnosis or an inadequate initial treatment. A young female patient with DFSP on the neck who was initially misdiagnosed as lipoma and then underwent inadequate initial resection is presented in this case.


Dermatofibrosarcoma protuberans Wide local excision Recurrence 


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Copyright information

© Association of Otolaryngologists of India 2018

Authors and Affiliations

  1. 1.TC Saglik Bakanlıgı Ankara Teaching and Research HospitalAnkaraTurkey
  2. 2.Ankara University School of MedicineAnkaraTurkey

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