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Enlarged Vestibular Aqueduct in Congenital Non-Syndromic Sensorineural Hearing Loss in Egypt

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

To estimate the frequency of isolated enlarged vestibular aqueduct (EVA) in patients with non-syndromic sensorineural hearing loss (SNHL) in an Egyptian population sample and to correlate its size with the degree of hearing loss. The study group comprised 16 patients (32 ears) suffering from non-syndromic SNHL since childhood. After a complete basic audiological evaluation, all patients were submitted to non contrast CT scan of the petrous bone in both axial & coronal planes. Vestibular aqueduct (VA) was measured at two points (midpoint & operculum) on right & left sides. The study group was divided according to VA size into three groups: group A, B and C. Group A included 6 ears (4 patients) with EVA, group B included 11 ears (7 patients) with borderline EVA and group C included 15 ears (9 patients) with normal VA size. There were no statistically significant differences between the three groups as regards laterality, degree of hearing loss and audiometric configuration. There was no correlation between VA midpoint & operculum and different variables (age and average pure tone thresholds). However, a significant correlation between VA midpoint & operculum was found. EVA was diagnosed in 6 out of 32 ears (18.75%) in the study sample. EVA size was not related to the degree of hearing loss or configuration. Despite the insignificant findings, moderate and high frequency sloping SNHL were considered the most common findings seen in patients with EVA.

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Authors and Affiliations

  1. Audio-Vestibular Unit of ENT Department, Kasr Al-Aini El-Manial University Hospital, Cairo University, Cairo, 11562, Egypt

    Maha Abou-Elew, Mostafa El-Khousht, Mohamed Sherif El-Minawi & Mona Selim

  2. Radiodiagnosis Department, Cairo University, Cairo, Egypt

    Ayman Ismail Kamel

Authors
  1. Maha Abou-Elew
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  2. Mostafa El-Khousht
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  3. Mohamed Sherif El-Minawi
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  4. Mona Selim
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  5. Ayman Ismail Kamel
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Correspondence to Maha Abou-Elew.

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Abou-Elew, M., El-Khousht, M., El-Minawi, M.S. et al. Enlarged Vestibular Aqueduct in Congenital Non-Syndromic Sensorineural Hearing Loss in Egypt. Indian J Otolaryngol Head Neck Surg 66 (Suppl 1), 88–94 (2014). https://doi.org/10.1007/s12070-011-0327-2

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