Abstract
A 4-year-old boy was diagnosed with hypertrophic cardiomyopathy with moderate degree of obstruction of the left ventricular outflow tract, secondary to asymmetric septal hypertrophy during infancy. Echocardiogram on follow-up showed increase in left ventricular outflow tract obstruction and appearance of an aneurysm in the membranous portion of interventricular septum. The appearance of the membranous septal aneurysm may be related to the direction of jet arising from the point of contact of the anterior mitral leaflet with the hypertrophied basal septum and hitting this part of the interventricular septum.
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Supplementary file1 (AVI 643 KB) Video 1 Modified parasternal long axis showing myxomatous mitral valve, moderate mitral regurgitation into the left atrium (LA), systolic anterior motion of the mitral valve, hypertrophied basal interventricular septum (IVS) and resultant turbulence in the left ventricular outflow tract and Aorta (AO)
Supplementary file2 (AVI 1115 KB) Video 2 Apical 4 chamber view showing membranous septal aneurysm (AN) protruding into the right ventricular inflow region and absence of any ventricular septal defect (LA, left atrium; LV, left ventricle; RA, right atrium; RV, right ventricle)
Supplementary file3 (AVI 17619 KB) Video 3 Simultaneous 2D and colour imaging of apical for chamber view showing contact of myxomatous mitral valve (AML) and hypertrophied basal interventricular septum (IVS) with resultant jet directed towards the membranous septal aneurysm (AN), absence of right ventricular inflow turbulence, and absence of interventricular shunt
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Arunakumar, P., Sastry, U.M., Satyamurthy, R.G. et al. Membranous septal aneurysm in a child with Noonan syndrome and hypertrophic cardiomyopathy. Indian J Thorac Cardiovasc Surg 38, 448–450 (2022). https://doi.org/10.1007/s12055-021-01287-x
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DOI: https://doi.org/10.1007/s12055-021-01287-x