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Isolated right pulmonary agenesis with dextrocardia presenting in adulthood

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Occurrence of right pulmonary agenesis in isolation is rare and carries a mortality rate of 50% during the first 5 years of life. The frequent association of congenital cardiac malformations with right pulmonary agenesis makes its prognosis bad. The diagnosis is challenging in those, who survive to adulthood because of nonspecific clinical presentations. Limited number of cases of isolated right pulmonary agenesis with dextrocardia in a structurally normal heart presenting in adulthood have been reported in the literature.

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Authors and Affiliations

  1. Department of Cardio-Thoracic and Vascular Surgery, SDS Tuberculosis Research Centre and Rajiv Gandhi Institute of Chest Diseses, Bengaluru, Karnataka, India

    Maruti Yamanappa Haranal & Shashidhar Buggi

  2. Department of Anesthesia, SDS Tuberculosis Research Centre and Rajiv Gandhi Institute of Chest Diseases, Bengaluru, Karnataka, India

    Satyaprakash Sanjeevaiah

Authors
  1. Maruti Yamanappa Haranal
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  2. Satyaprakash Sanjeevaiah
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  3. Shashidhar Buggi
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Correspondence to Maruti Yamanappa Haranal.

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The authors declare that they have no conflict of interest.

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All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

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Informed consent was obtained from the individual participant included in the study.

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Haranal, M.Y., Sanjeevaiah, S. & Buggi, S. Isolated right pulmonary agenesis with dextrocardia presenting in adulthood. Indian J Thorac Cardiovasc Surg 34, 173–176 (2018). https://doi.org/10.1007/s12055-017-0570-6

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  • DOI: https://doi.org/10.1007/s12055-017-0570-6

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