Abstract
Aneurysm of the ascending aorta with coarctation of the aorta is a rare find in the literature. We report a case of a huge ascending aorta aneurysm in a patient of Marfan’s syndrome and associated coarctation of the aorta. The patient underwent staged procedure in the form of balloon dilatation for the coarctation of the aorta and a successful Bentall procedure for the aneurysm of the aorta with a brief period of deep hypothermic circulatory arrest (DHCA). Two-staged approach is the ideal management for such cases amenable for endovascular repair.
Similar content being viewed by others
References
Alexiou C, Langley SM, Charlesworth P, Haw MP, Livesey SA, Monro JL. Aortic root replacement in patients with Marfan’s syndrome: the Southampton experience. Ann Thorac Surg. 2001;72:1502–8.
Rowinski O, Wojtaszek M, Milczarek K, Cieszanowski A, Szmidt J. Unusual presentation of aortic disease in Marfan syndrome: case report. Int J Cardiol. 2008;127:e61–3.
Mckusick VA. The cardiovascular aspects of Marfan’s syndrome: a heritable disorder of connective tissue. Circulation. 1955;11:321–42.
Abbott ME. Coarctation of the aorta of the adult type. Am Heart J. 1928;3:574–8.
Roberts WC, Honig HS. The spectrum of cardiovascular disease in the Marfan syndrome: a clinico-morphologic study of 18 necropsy patients and comparison to 151 previously reported necropsy patients. Am Heart J. 1982;104:115–35.
Pyeritz RE. The Marfan syndrome. Annu Rev Med. 2000;51:481–510.
Gott VL, Laschinger JC, Cameron DE, et al. The Marfan syndrome and the cardiovascular surgeon. Eur J Cardiothorac Surg. 1996;10:159–68.
Sampath R, O'Connor WN, Noonan JA, Todd EP. Management of ascending aortic aneurysm complicating coarctation of the aorta. Ann Thorac Surg. 1982;34:125–31.
Kothari J, Brahmbhatt B, Baria K, Patel J. Different strategies for simultaneous repair of aortic coarctation and associated cardiac diseases in adult patients. Int J Med Sci Pub Health. 2016;5:186–90.
Vijayanagar R, Natarajan P, Eckstein PF, Bognolo DA, Toole JC. Aortic valvular insufficiency and postductal aortic coarctation in the adult. Combined surgical management through median sternotomy: a new surgical approach. J Thorac Cardiovasc Surg. 1980;79:266–8.
Author information
Authors and Affiliations
Corresponding author
Ethics declarations
Funding
This study has not been funded by any party whatsoever.
Conflict of interest
The authors declare that they have no conflict of interest.
Ethical approval
This article does not contain any studies with animals performed by any of the authors.
All procedures performed in study involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.
Informed consent
Informed consent was obtained from all individual participants included in the study. Additional informed consent was obtained from all individual participants for whom identifying information is included in this article.
Rights and permissions
About this article
Cite this article
Satyarthy, S., Roy, A., Gupta, U. et al. Incidental finding of coarctation of the aorta in a Marfan patient: a case report. Indian J Thorac Cardiovasc Surg 34, 157–160 (2018). https://doi.org/10.1007/s12055-017-0564-4
Received:
Revised:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s12055-017-0564-4