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Pentalogy and Cantrell and sternal cleft: a report of two cases and review of literature

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

An Erratum to this article was published on 08 May 2017

This article has been updated

Abstract

Pentalogy of Cantrell refers to a clinical entity seen in children, with attendant impact on quality of life, if early intervention is not given. We report two cases who presented to our hospital, Fortis hospital Mulund, Mumbai. The first had a sternal cleft with partial ectopia thoracic while the second case had a type 3 Pentalogy of Cantrell. Computerized axial tomography (CT scan) confirmed the diagnosis. Both had surgical repair with a very good outcome.

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Change history

  • 08 May 2017

    An erratum to this article has been published.

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Authors and Affiliations

  1. College of Medicine, Department of Pediatrics, University of Nigeria/University of Nigeria Teaching Hospital (UNTH), Ituku-Ozalla, Enugu State, Nigeria

    Josephat Maduabuchi Chinawa

  2. Fortis Hospital limited, Mulund Goregaon Link Road, Bhandup (West), Mumbai, India

    Vijay Agarwal, Swati Garekar, Sarang Gaikwad & Bhadra Trivedi

Authors
  1. Josephat Maduabuchi Chinawa
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  2. Vijay Agarwal
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  3. Swati Garekar
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  4. Sarang Gaikwad
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  5. Bhadra Trivedi
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Corresponding author

Correspondence to Josephat Maduabuchi Chinawa.

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Funding

This study was not funded by any organization. We bore all the expense that accrued from the study.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standard.

Conflict of interest

The authors declare that they have no competing interests.

Informed consent

Informed consent was obtained from all individual participants.

Additional information

An erratum to this article is available at https://doi.org/10.1007/s12055-017-0550-x.

Electronic supplementary material

Video 1

Showing surgical procedure in the closure of Case 1. (3GP 5441 kb)

Video 2

Showing ectopia cordis abdominis in the index patient. (MP4 18,719 kb)

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Chinawa, J.M., Agarwal, V., Garekar, S. et al. Pentalogy and Cantrell and sternal cleft: a report of two cases and review of literature. Indian J Thorac Cardiovasc Surg 33, 237–239 (2017). https://doi.org/10.1007/s12055-017-0525-y

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  • DOI: https://doi.org/10.1007/s12055-017-0525-y

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