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A case of pedunculated right ventricular fibroma: a rare presentation and review of literature

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Cardiac fibromas are rare benign tumors which are found mainly in children and sometimes reported in adults. These are usually intramyocardial solid tumors, located mostly within the left ventricular free wall and interventricular septum. Rarely, they may be found in the right ventricle. We present a rare pedunculated fibroma attached to the interventricular septum in the region of the subpulmonary infundibulum in the right ventricular outflow tract in an 8-year-old girl who had presented with gradually increasing exertional chest pain over 8 months without any weight loss, fever, and anemia. Echocardiography showed a pedunculated freely mobile right ventricular mass moving into the main pulmonary artery during systolic contraction. The most likely diagnosis was a myxoma. It was excised through pulmonary arteriotomy under cardiopulmonary bypass. On histopathological examination, it was confirmed as a fibroma. The patient is doing well after 7 years follow-up without any recurrence.

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Authors and Affiliations

  1. Department of Cardiothoracic Surgery, Medical College Kolkata, 88, College Street, Kolkata, West Bengal, 700073, India

    Kallol Dasbaksi, Mohammad Zahid Hossain, Suranjan Haldar & Plaban Mukherjee

  2. 23, New Santoshpur 1st Lane, East Jadavpur, Kolkata, 700075, India

    Kallol Dasbaksi

Authors
  1. Kallol Dasbaksi
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  2. Mohammad Zahid Hossain
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  3. Suranjan Haldar
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  4. Plaban Mukherjee
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Contributions

All the authors have contributed to the study concept, design, data collection, data analysis for interpretation, for writing this manuscript.

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Correspondence to Kallol Dasbaksi.

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The authors declare that they have no conflict of interest.

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This study did not receive any funding.

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All procedures performed in study were in accordance with the ethical standards of the institutional and national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

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Informed consent was obtained from the guardians of the patient to publish this report for academic interest.

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Dasbaksi, K., Hossain, M.Z., Haldar, S. et al. A case of pedunculated right ventricular fibroma: a rare presentation and review of literature. Indian J Thorac Cardiovasc Surg 33, 261–264 (2017). https://doi.org/10.1007/s12055-017-0509-y

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  • DOI: https://doi.org/10.1007/s12055-017-0509-y

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