Abstract
Aortic valve diseases are most commonly caused by degenerative changes, congenital malformation and rheumatic affection of valves. A very rare cause is the deposition of foreign material in the valvular tissues as a result of alkaptonuria. In this case report, we present a case of alkaptonuric ochronosis of congenital bicuspid aortic valve, presented with severe aortic valve stenosis and treated with aortic valve replacement surgery.
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Parashi, H.S., Joshi, M.M., Jadhao, M.R. et al. Alkaptonuric ochronosis of congenital bicuspid aortic valve—a case report. Indian J Thorac Cardiovasc Surg 33, 155–158 (2017). https://doi.org/10.1007/s12055-017-0487-0
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DOI: https://doi.org/10.1007/s12055-017-0487-0