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Adenocarcinoma Ex-goblet Cell Carcinoid of the Appendix: a Case Report and Overview of the Disease

  • Uroosa Ibrahim
  • Gautam Valecha
  • Gwenalyn Garcia
  • Amina Saqib
  • Monika Wrzolek
  • Meekoo Dhar
Case Report
  • 129 Downloads

Introduction

Goblet cell carcinoid (GCC) of the appendix is a rare disease with varying guidelines for histopathologic diagnosis and management. The disease is intriguing in terms of its pathologic features. Three subtypes have been described depending on the presence of signet ring cells and extent of differentiation of the adenocarcinoma component [1]. The clinical behavior of the tumor ranges from aggressive to relatively indolent disease. Treatment is based on extent of the disease, grade of the tumor, and individual patient characteristics. Whereas surgical resection remains the mainstay of resectable disease, adjuvant chemotherapy and intraperitoneal chemotherapy have been employed. We discuss our experience with diagnosis and management of the disease in a patient we encountered.

Case

A 47-year-old female presented to the emergency room with complaints of ongoing abdominal pain for 2 weeks. The patient had no medical problems and had not had any surgical procedures in the past....

Keywords

Signet Ring Cell Intraperitoneal Chemotherapy Architectural Distortion Cell Carcinoid Appendiceal Tumor 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Notes

Compliance with Ethical Standards

This study did not require funding.

Conflict of Interest

The authors declare that they have no conflict of interest.

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Copyright information

© Springer Science+Business Media New York 2017

Authors and Affiliations

  1. 1.Department of Hematology/OncologyStaten Island University HospitalNew YorkUSA
  2. 2.Department of Pulmonary and Critical Care MedicineStaten Island University HospitalNew YorkUSA
  3. 3.Department of PathologyStaten Island University HospitalNew YorkUSA

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