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Nested Stromal Epithelial Tumor of the Liver—Liver Transplantation and Follow-Up

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Abstract

Background

The nested stromal epithelial tumor (NSET) of the liver is a rare tumor entity which is being reported in young girls.

Case Report

In our 16-year-old female patient, we have performed a liver transplantation (LTX) for a non-metastasizing non-resectable liver tumor. The patient was tumor free in the follow-up. At 28 months postoperatively, we detected lung metastases in the F18-FDG-PET/CT. The patient died 37 months after LTX from progressive pulmonary metastases.

Conclusion

LTX should not have been generally recommended for NSET. Further statements about the value of LTX for NSET will be possible only after evaluation of the course of the disease in a larger number of transplanted patients.

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Abbreviations

NSET:

Nested stromal epithelial tumor

LTX:

Liver transplantation

CT:

Computed tomography

MRI:

Magnetic resonance imaging

PET/CT:

Positron emission tomography

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Correspondence to Merten Hommann.

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Hommann, M., Kaemmerer, D., Daffner, W. et al. Nested Stromal Epithelial Tumor of the Liver—Liver Transplantation and Follow-Up. J Gastrointest Canc 42, 292–295 (2011). https://doi.org/10.1007/s12029-010-9248-7

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  • DOI: https://doi.org/10.1007/s12029-010-9248-7

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