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Carney’s Triad: Case Report and Review

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Abstract

Introduction

Carney’s triad is a rare pathogenic entity which consists of the association in young women of multiple condromatosis in the lung, gastric leiomyosarcoma, and extradrenal paraganglioma; although the presence of three at the same time is not required for its diagnosis.

Case Report

We present the case of a 27-year-old woman who was diagnosed of pulmonary multiple hamartomatosis and gastric stromal tumor.

Discussion

A review of the literature shows the most important prognosis factors and therapeutic options. Surgery for gastrointestinal stromal tumors and extradrenal paraganglioma seems to be the best treatment up to date.

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Authors and Affiliations

  1. General and Digestive Surgery, Hospital Reina Sofía, Avd. Menéndez Pidal s/n, Córdoba, Spain

    R. Díaz Nieto, A. Arjona Sánchez, M. Gómez Álvarez, D. Martínez Cecilia, J. M. Sánchez Hidalgo, R. Ciria Bru, M. C. Pérez Manrique, J. Sánchez Rodríguez & S. Rufián Peña

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  1. R. Díaz Nieto
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  2. A. Arjona Sánchez
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  3. M. Gómez Álvarez
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  4. D. Martínez Cecilia
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  5. J. M. Sánchez Hidalgo
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  6. R. Ciria Bru
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  7. M. C. Pérez Manrique
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  8. J. Sánchez Rodríguez
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  9. S. Rufián Peña
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Correspondence to R. Díaz Nieto.

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Díaz Nieto, R., Arjona Sánchez, A., Gómez Álvarez, M. et al. Carney’s Triad: Case Report and Review. J Gastrointest Canc 38, 137–140 (2007). https://doi.org/10.1007/s12029-008-9026-y

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