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Arrhythmogenic right ventricular dysplasia

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Opinion statement

Despite recurrences of ventricular tachycardia, patients with arrhythmogenic right ventricular dysplasia have a favorable prognosis with medical therapy. Because of the low incidence of arrhythmic death and the problems involved in identifying patients at high risk, it is difficult to evaluate the benefits of interventional therapies (ablation, surgery, and implantable cardioverter-defibrillators).

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Trohman, R.G., Sahu, J. Arrhythmogenic right ventricular dysplasia. Curr Treat Options Cardio Med 1, 259–268 (1999). https://doi.org/10.1007/s11936-999-0042-4

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