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Modern Management of Bladder Exstrophy Repair

  • Pediatric Urology (M Castellan and R Gosalbez, Section Editors)
  • Published:
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Abstract

The exstrophy–epispadias complex is a rare congenital malformation of the genitourinary system, abdominal wall musculature, and pelvic bones. Historically, surgical outcomes in patients with classic bladder exstrophy, the most common presentation of the exstrophy–epispadias complex, were poor. However, modern techniques have increased the success of achieving urinary continence, satisfactory cosmesis, and improved quality of life. Still, recent studies recognize complications that may occur during management of these patients. This review provides readers with an overview of the exstrophy–epispadias complex, the modern management of bladder exstrophy, and potential surgical complications.

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Abbreviations

EEC:

Exstrophy–epispadias complex

CBE:

Classic bladder exstrophy

OEIS:

Omphalocele, exstrophy, imperforate anus, spinal abnormalities

VUR:

Vesicoureteral reflux

MRI:

Magnetic resonance imaging

CIC:

Clean intermittent catheterization

MSRE:

Modern staged repair of exstrophy

CPRE:

Complete primary repair of exstrophy

BNR:

Bladder neck reconstruction

CUD:

Continent urinary diversion

References

Papers of particular interest, published recently, have been highlighted as: • Of importance •• Of major importance

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Conflict of Interest

Dr. Brian M. Inouye reported no potential conflicts of interest relevant to this article.

Dr. Eric Z. Massanyi reported no potential conflicts of interest relevant to this article.

Dr. Heather Di Carlo reported no potential conflicts of interest relevant to this article.

Dr. Bhavik B. Shah reported no potential conflicts of interest relevant to this article.

Dr. John P. Gearhart reported no potential conflicts of interest relevant to this article.

Human and Animal Rights and Informed Consent

This article does not contain any studies with human or animal subjects performed by any of the authors.

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Authors and Affiliations

  1. James Buchanan Brady Urological Institute, Division of Pediatric Urology, Charlotte Bloomberg Children’s Hospital, The Johns Hopkins University School of Medicine, 1800 Orleans St. Suite 7304, Baltimore, MD, 21287, USA

    Brian M. Inouye, Eric Z. Massanyi, Heather Di Carlo, Bhavik B. Shah & John P. Gearhart

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  1. Brian M. Inouye
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  2. Eric Z. Massanyi
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  3. Heather Di Carlo
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  4. Bhavik B. Shah
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  5. John P. Gearhart
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Correspondence to John P. Gearhart.

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Inouye, B.M., Massanyi, E.Z., Di Carlo, H. et al. Modern Management of Bladder Exstrophy Repair. Curr Urol Rep 14, 359–365 (2013). https://doi.org/10.1007/s11934-013-0332-y

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