Current Pain and Headache Reports

, Volume 15, Issue 4, pp 280–288 | Cite as

Uncommon Headache Syndromes in the Pediatric Population

  • Marco A. Arruda
  • Regina C. A. P. Albuquerque
  • Marcelo E. Bigal


Headache is one of the most common symptoms in children and adolescents, and headache syndromes are an important reason for medical consulting. According to the second edition of the International Classification of Headache Disorders, there are 196 possible headache diagnoses, of which 113 have been described in pediatric population. Herein, we focus on unusual pediatric headache syndromes. We group them as headaches with migraine features, short-duration headaches with autonomic features, short-duration headaches without autonomic features, and potentially ominous forms of headaches. Although rare as single entities, providers focusing on pediatric headaches certainly will face some of these headaches and need to be comfortable on the diagnostic approach.


Headache Facial pain Cranial neuralgias Cluster headache Paroxysmal hemicranias Stabbing headache Retinal migraine Ophthalmoplegic migraine Trigeminal neuralgias Trigeminal autonomic cephalalgias Etiology Diagnosis Classification International Classification of Headache Disorders, second edition ICHD-II Childhood Adolescence 


Papers of particular interest, published recently, have been highlighted as: • Of importance •• Of major importance

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Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  • Marco A. Arruda
    • 1
  • Regina C. A. P. Albuquerque
    • 2
  • Marcelo E. Bigal
    • 3
    • 4
  1. 1.Glia InstituteChild and Adolescent NeurologyRibeirão PretoBrazil
  2. 2.São José do Rio Preto School of MedicineSão José do Rio PretoBrazil
  3. 3.Merck Research LaboratoriesWhitehouse StationUSA
  4. 4.Department of NeurologyAlbert Einstein College of MedicineBronxUSA

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