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Long-term outcomes following partial atrioventricular septal defect (AVSD) repair in Ireland

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Abstract

Background

We describe the long-term results of partial atrioventricular septal defect (AVSD) repair in a single centre encompassing a 22-year period. Described are rates of survival, reoperation and complications.

Methods

We performed a retrospective review of 556 patients undergoing AVSD repair to identify the 51 patients who underwent partial AVSD repair in Our Lady’s Children’s Hospital, Crumlin, Ireland, between 1993 and 2015 with long-term follow-up where available.

Results

A total of 29 (56.8%) of patients were male and mean age at operation was 3.32 years. Mean weight was 13.2 kg. Trisomy 21 was present in 29 (56.8%). Five patients (9.6%) had undergone prior surgery. Mean cardiopulmonary bypass time was 89 ± 36 min and mean aortic cross-clamp time was 57 ± 28 min. One patient underwent partial AVSD repair and concomitant tracheal resection and extracorporeal membrane oxygenation decannulation. One patient was managed with suture atrial septal defect (ASD) closure, the remainder with patch repair of ASD and mitral cleft closure. The length of hospital stay was 9 ± 5 days. Median follow-up was 6.06 years (IQR, 1.65–10.2 years). There were no early mortalities. One patient died 1 year following surgery (1.9%). One patient required reoperation at an interval of 2 years for severe mitral regurgitation (1.9%).

Conclusions

Short- and long-term survival following partial AVSD repair in Ireland revealed excellent results compared with other published series. Reoperation incidence also compared excellently with other reports published in the literature.

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Correspondence to Katie E. O’ Sullivan.

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Ethical approval was sought and granted by the institutional ethics committee in Our Lady’s Children’s Hospital, Crumlin.

Conflict of interest

The authors declare that they have no conflicts of interest.

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O’ Sullivan, K.E., Fleck, R., Vigano, G. et al. Long-term outcomes following partial atrioventricular septal defect (AVSD) repair in Ireland. Ir J Med Sci 188, 475–479 (2019). https://doi.org/10.1007/s11845-018-1855-5

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  • DOI: https://doi.org/10.1007/s11845-018-1855-5

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