Abstract
Background
A congenital diaphragmatic hernia (Bochdalek’s hernia) rarely presents in adulthood.
Case presentation
We present the case of a 21-year-old woman with thrombocytopenia secondary to hypersplenism due to left-sided (sinistral) portal hypertension. This portal hypertension was caused by strangulation of the spleen within a Bochdalek’s hernia. Subacute gastric volvulus compounded by portal hypertensive gastropathy resulted in her presentation with acute haematemesis.
Conclusions
Congenital diaphragmatic hernias may present in the adult. Their presentation is variable, and they may produce life-threatening complications.
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Acknowledgments
We would like to thank our patient for her consent for presenting this case. The authors report no funding source.
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The authors report no conflict of interest.
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Kennedy, R., Donaghy, A., Ahmad, J. et al. Portal hypertension and hypersplenism in a patient with a Bochdalek hernia: a case report. Ir J Med Sci 178, 111–113 (2009). https://doi.org/10.1007/s11845-008-0140-4
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DOI: https://doi.org/10.1007/s11845-008-0140-4