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Repeated aortic dissection in a patient with autosomal dominant polycystic kidney disease

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Abstract

Autosomal dominant polycystic kidney disease is a systemic disorder associated with cardiovascular complications. However, there are few reports on autosomal dominant polycystic kidney disease-associated aortic dissection. Herein, we present a rare case of a 46-year-old man with autosomal dominant polycystic kidney disease who underwent endovascular repair for acute type B aortic dissection three years after his initial open surgery for acute type A aortic dissection. The postoperative course was uneventful, and he is doing well two years after the endovascular repair. Clinicians should be aware of the potential for occurrence of aortic dissection in patients with autosomal dominant polycystic kidney disease, including the possibility of recurrence.

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Acknowledgements

We thank Editage (http://www.editage.jp) for English language editing. We also thank Dr. Takumi Kitaoka for the histopathological consultation.

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Correspondence to Kimihiro Kobayashi.

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Kobayashi, K., Kuroda, Y., Nakai, S. et al. Repeated aortic dissection in a patient with autosomal dominant polycystic kidney disease. Gen Thorac Cardiovasc Surg 70, 390–393 (2022). https://doi.org/10.1007/s11748-021-01756-5

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  • DOI: https://doi.org/10.1007/s11748-021-01756-5

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