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Isolated left subclavian artery with right aortic arch: case report and literature review of 50 cases

General Thoracic and Cardiovascular Surgery volume 69, pages 885–889 (2021)Cite this article

Abstract

Isolated left subclavian artery (ILSA) with right aortic arch is a rare vascular anomaly accounting for 0.8% in all right-sided aortic arch anomalies. We report a case of an isolated left subclavian artery with right aortic arch and a combination of subclavian as well as pulmonary steal in infant with Tetralogy of Fallot. We reviewed and summarized 50 similar cases reported in the literature over the last 30 years, in order to gain a thorough understanding of this rare anomaly.

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Funding

This research received no specific grant from any funding agency, commercial or not-for-profit sectors.

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Affiliations

  1. Department of Cardiac Sciences, College of Medicine, King Saud University, P. O. Box 7805, Riyadh, 11472, Saudi Arabia

    Abdullah N. Alhuzaimi

  2. Heart Center, King Faisal Specialist Hospital & Research Center, Riyadh, Saudi Arabia

    Abdullah N. Alhuzaimi & Mamdouh AlAhmadi

  3. Department of Pediatrics, King Faisal Specialist Hospital & Research Center, Riyadh, Saudi Arabia

    Khalifah A. Aldawsari

Authors
  1. Abdullah N. Alhuzaimi
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  2. Khalifah A. Aldawsari
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  3. Mamdouh AlAhmadi
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Correspondence to Abdullah N. Alhuzaimi.

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Supplementary Information

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Supplementary file2 Online Resource Video 1: Aortography showed right aortic arch, late filling of isolated left subclavian artery and pulmonary artery through PDA (MPG 5046 KB)

Supplementary file3 Online Resource Video 2: Right subclavian artery angiogram showed numerous small connections from the right vertebral artery through head and neck vessels to LVA to supply the ILSA with significant flow into the pulmonary arteries (MPG 3938 KB)

Supplementary file4 Online Resource Video 3: ILSA angiogram showed it is connected to the pulmonary artery through a left PDA (MPG 3936 KB)

11748_2020_1564_MOESM1_ESM.xlsx

Supplementary file1 Online Resources Table S: Summery of Case Reports of Isolated Left Subclavian Artery with Right Aortic Arch in Medical Literature from 1990-2020 (n=50) (XLSX 19 KB)

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Alhuzaimi, A.N., Aldawsari, K.A. & AlAhmadi, M. Isolated left subclavian artery with right aortic arch: case report and literature review of 50 cases. Gen Thorac Cardiovasc Surg 69, 885–889 (2021). https://doi.org/10.1007/s11748-020-01564-3

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  • DOI: https://doi.org/10.1007/s11748-020-01564-3

Keywords

  • Isolated subclavian
  • Pulmonary steal
  • Subclavian steal syndrome
  • Right aortic arch
  • Vertebrobasilar insufficiency