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A rare resected case of pulmonary rhabdomyosarcoma

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Abstract

Rhabdomyosarcoma is a well-known neoplasm in children that frequently occurs in the extremities, the head and neck region, and the genitourinary tract. To the best of our knowledge, pulmonary primary rhabdomyosarcoma in adults is exceedingly rare, and few resected cases have been reported. We report a case of pulmonary primary rhabdomyosarcoma that was surgically resected then treated with adjuvant chemotherapy (vincristine, actinomycin-D and cyclophosphamide). At 9 months after surgery, the patient is free from disease. Although the prognosis of rhabdomyosarcoma is unfavorable, surgical resection and adjuvant therapy could be a potential treatment strategy for pulmonary primary rhabdomyosarcoma.

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Authors and Affiliations

  1. Division of Chest Surgery, Hyogo Cancer Center, 13-70, Kitaoji-cho, Akashi, Japan

    Yuki Nishioka, Shinya Tane, Wataru Nishio, Hiroki Tanaka, Hiroyuki Ogawa, Yoshitaka Kitamura & Masahiro Yoshimura

  2. Division of Pathology, Hyogo Cancer Center, 13-70, Kitaoji-cho, Akashi, Japan

    Toshiko Sakuma

Authors
  1. Yuki Nishioka
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  2. Shinya Tane
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  3. Wataru Nishio
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  4. Hiroki Tanaka
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  5. Hiroyuki Ogawa
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  6. Yoshitaka Kitamura
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  7. Toshiko Sakuma
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  8. Masahiro Yoshimura
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Nishioka, Y., Tane, S., Nishio, W. et al. A rare resected case of pulmonary rhabdomyosarcoma. Gen Thorac Cardiovasc Surg 67, 1089–1092 (2019). https://doi.org/10.1007/s11748-019-01086-7

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  • DOI: https://doi.org/10.1007/s11748-019-01086-7

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