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Aortic root remodeling in a patient with Turner syndrome using the reference curves of aortic diameters in children

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Abstract

We report the successful surgical treatment of aortic regurgitation in a 27-year-old woman with Turner syndrome (TS) who was admitted with exacerbation of dyspnea on exertion. Echocardiography showed a bicuspid aortic valve with severe aortic regurgitation and computed tomography showed dilatation of the ascending aorta and aortic root. Due to the patient’s low body surface area (due to TS), standard determination of aortic size was not possible; therefore, we used the reference curves of aortic diameters in children. Because of the possibility of fatal ascending aortic dissection and rupture, we performed concomitant aortic root remodeling and aortic valve repair.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Osaka City General Hospital, 2-13-22 Miyakojimahondori, Miyakojima-ku, Osaka, 534-0021, Japan

    Goki Inno, Yosuke Takahashi, Yasuyuki Kato & Yasuyuki Sasaki

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  1. Goki Inno
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  2. Yosuke Takahashi
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  3. Yasuyuki Kato
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  4. Yasuyuki Sasaki
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Correspondence to Goki Inno.

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Inno, G., Takahashi, Y., Kato, Y. et al. Aortic root remodeling in a patient with Turner syndrome using the reference curves of aortic diameters in children. Gen Thorac Cardiovasc Surg 66, 667–670 (2018). https://doi.org/10.1007/s11748-018-0889-y

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  • DOI: https://doi.org/10.1007/s11748-018-0889-y

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