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Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome

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Abstract

We report a patient with vascular-type Ehlers–Danlos syndrome (vEDS) who developed pneumothorax and was treated with a total pleural covering technique (TPC). A 24-year-old man developed repeat pneumothorax with intermittent hemo-sputum. Based on unusual radiological manifestations of lung lesions and physical findings, EDS was suspected as an underlying cause of the pneumothorax. Surgical treatment was performed using a mediastinal fat pad and TPC, and no relapse was seen up to 2 years after surgery. TPC is a less invasive surgical approach for selected patients with vEDS. Accurate underlying diagnosis of vEDS and systemic evaluation of vascular complications are necessary before planning surgery.

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Acknowledgments

We gratefully acknowledge the assistance of Dr. Atsushi Hatamochi, Dokkyou Medical University, with the electron microscopic and biochemical analyses of type III procollagen production.

Conflict of interest

All authors have declared no competing interest.

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Authors and Affiliations

  1. Department of General Thoracic Surgery, Osaka Prefectural Medical Center for Respiratory and Allergic Diseases, 3-7-1 Habikino, Habikino, Osaka, Japan

    Yoshihisa Kadota, Eriko Fukui, Naoto Kitahara, Eiji Okura & Mitsunori Ohta

Authors
  1. Yoshihisa Kadota
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  2. Eriko Fukui
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  3. Naoto Kitahara
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  4. Eiji Okura
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  5. Mitsunori Ohta
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Correspondence to Yoshihisa Kadota.

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Kadota, Y., Fukui, E., Kitahara, N. et al. Total pleural covering technique for intractable pneumothorax in patient with Ehlers–Danlos syndrome. Gen Thorac Cardiovasc Surg 64, 425–428 (2016). https://doi.org/10.1007/s11748-014-0504-9

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  • DOI: https://doi.org/10.1007/s11748-014-0504-9

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