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Lymphatic and venous malformation or “lymphangiohemangioma“ of the anterior mediastinum: case report and literature review

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Lymphatic and venous malformations (LVM) are tumor-like lesions combining dysplastic lymphatic and venous vessel structures. They are rarely found in the mediastinum. We present a case of mediastinal LVM, with review of the literature. An asymptomatic 60-yearold man presented for evaluation of an anterior mediastinal mass. On chest computed tomography (CT), the mass demonstrated contrast enhancement and its 7-mm vein draining directly into the left brachiocephalic vein. The tumor was resected completely using video-assisted thoracoscopic surgery. The surgical specimen revealed combined features of venous and lymphatic dysplasia, and was diagnosed it as LVM, so-called mediastinal lymphangiohemangioma. Management plans based on precise imaging studies using magnetic resonance imaging and multi-detector-row CT phlebography could be helpful in guiding both preoperative diagnosis and subsequent treatment decisions for mediastinal LVM.

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Correspondence to Yoshihisa Kadota.

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Kadota, Y., Utsumi, T., Kawamura, T. et al. Lymphatic and venous malformation or “lymphangiohemangioma“ of the anterior mediastinum: case report and literature review. Gen Thorac Cardiovasc Surg 59, 575–578 (2011).

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