Abstract
Angiosarcoma is a rare neoplasm, accounting for only 1%–2% of all sarcomas. It occurs most frequently in the skin and soft tissue and rarely in the thoracic region. To our knowledge, a mediastinal angiosarcoma is extremely rare. We report on the surgical resection of a rare case of giant epithelioid angiosarcoma originating in the anterior mediastinum, followed by six courses of adjuvant chemotherapy (doxorubicin + ifosfamide). The patient is alive and asymptomatic 1 year after surgery. As the prognosis for unresectable cases is generally dismal, surgical resection and adjuvant therapy can be an option for mediastinal angiosarcoma.
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Tane, S., Tanaka, Y., Tauchi, S. et al. Radically resected epithelioid angiosarcoma that originated in the mediastinum. Gen Thorac Cardiovasc Surg 59, 503–506 (2011). https://doi.org/10.1007/s11748-010-0710-z
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DOI: https://doi.org/10.1007/s11748-010-0710-z