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Obesity Surgery

, Volume 18, Issue 10, pp 1313–1317 | Cite as

Launois-Bensaude Syndrome: An Unusual Localization of Obesity Disease

  • Giovanni Verna
  • Nicola Kefalas
  • Filippo BorianiEmail author
  • Salvatore Carlucci
  • Ingrid Choc
  • Maria Alessandra Bocchiotti
Research Article

Abstract

Background

Launois-Bensaude syndrome is a rare pathology consisting of adipose masses symmetrically distributed mainly in the superior part of the body. Men are especially affected between age of 30 and 60 as well as chronic alcohol abusers. Etiopathogenesis is attributable to mutations or deletions of mitochondrial DNA, and alcohol is a possible cofactor.

Methods

The current treatment of the disease is described based on the authors’ experience. Four cases treated in our department are retrospectively reviewed regarding comorbidities and type of surgery performed.

Results

A relevant and long-lasting reduction of fat bulges has been obtained in all cases with no major complications except for a mild anemia.

Conclusion

Launois-Bensaude syndrome causes a functional rather than esthetic concern due to the peculiar localization of fat bulges. Currently, the only effective therapy is surgery, through lipectomy or liposuction of adipose bulges.

Keywords

Launois-Bensaude syndrome Madelung disease Benign symmetrical lipomatosis 

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Copyright information

© Springer Science + Business Media, LLC 2008

Authors and Affiliations

  • Giovanni Verna
    • 1
  • Nicola Kefalas
    • 1
  • Filippo Boriani
    • 1
    • 2
    Email author
  • Salvatore Carlucci
    • 1
  • Ingrid Choc
    • 1
  • Maria Alessandra Bocchiotti
    • 1
  1. 1.Department of Plastic Reconstructive and Aesthetic SurgeryUniversity of TurinTurinItaly
  2. 2.Istituto di Chirurgia PlasticaUniversità di TorinoTorinoItaly

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