Abstract
Introduction
Extraskeletal Ewing’s sarcoma is reported in the medical literature, but none has been described as presenting with a resectable liver mass.
Methods
A case of a 29-year-old male patient who presented with a large symptomatic mass in the right lobe of the liver which, following resection, demonstrated the characteristic histopathology and fusion protein (EWSR1-Fli1) found in Ewing’s sarcoma was reported.
Discussion
Complete surgical resection offers the best long-term outlook. Cure rates with appropriate surgical and chemotherapeutic management range between 30 and 60 %.
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McGrann, P.F., Pooleman, I.J., Wilson, C.H. et al. Primary Hepatic Ewing’s Sarcoma with Cytogenetic Confirmation. J Gastrointest Surg 18, 635–637 (2014). https://doi.org/10.1007/s11605-013-2284-4
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DOI: https://doi.org/10.1007/s11605-013-2284-4