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Adrenal pheochromocytoma: is it all or the tip of the iceberg?

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Abstract

Adrenal pheochromocytoma is not always a simple retroperitoneal tumor but may be part of a more complicated condition. It often has a spectrum of complex and variable imaging features, may present as a collision tumor and composite tumor, and is associated with a variety of clinical syndromes. A comprehensive understanding of the clinical, pathological, and variable imaging manifestations of pheochromocytoma can help radiologists make an accurate diagnosis. This article reviews various special imaging features of pheochromocytoma and pheochromocytoma-related diseases.

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Acknowledgements

We thank Dr. Lili CHEN, Department of Pathology, The First Affiliated Hospital of Sun Yat-Sen University, for advice on pathological images. We thank Dr. Yuanxian YANG, Department of obstetrics and gynecology, the Eighth Hospital of Wuhan, for her encouragement that let us never give up.

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No funding was received to assist with the preparation of this manuscript.

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Author notes

  1. Ke Wang and Guanglei Tang contributed equally to this work, and they are co-first authors.

Authors and Affiliations

  1. Department of Radiology, The First Affiliated Hospital of Sun Yat-Sen University, No. 58 Zhongshanerlu Road, Guangzhou, 510080, Guangdong, People’s Republic of China

    Ke Wang, Guanglei Tang, Yang Peng, Chang Li, Wenhao Fu, Ruixi Li & Jian Guan

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  1. Ke Wang
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Contributions

KW and GT contributed equally to this work. They are co-first authors. All authors contributed to the study conception and design. The first draft of the manuscript was written by KW and GT. All authors commented on previous versions of the manuscript. All authors read and approved the final manuscript.

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Correspondence to Jian Guan.

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The manuscript is a review article and has no studies with human participants or animals performed by any of the authors. Approval was granted by the Ethics Committee of The First Affiliated Hospital, Sun Yat-Sen University.

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Wang, K., Tang, G., Peng, Y. et al. Adrenal pheochromocytoma: is it all or the tip of the iceberg?. Jpn J Radiol 40, 120–134 (2022). https://doi.org/10.1007/s11604-021-01199-1

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  • DOI: https://doi.org/10.1007/s11604-021-01199-1

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