HSS Journal

, Volume 4, Issue 1, pp 81–86 | Cite as

Anti-neutrophil Cytoplasmic Antibody (c-ANCA) Positive Recurrent Eosinophilic Fasciitis Responsive to Cyclophosphamide

A Clinical Pathology Conference Held by the Division of Rheumatology at Hospital for Special Surgery
  • Virginia Florina Haiduc
  • Doruk Erkan
  • Kyriakos Kirou
  • Sherri Birchansky
  • Josephine Park
  • Moris J. Danon
 

Key words

eosinophilic fasciitis cyclophosphamide necrotizing vasculitis 

Abbreviations

ANA

Antinuclear antibodies

c-ANCA

Cytoplasmic antineutrophil cytoplasmic antibody

CRP

C-reactive protein

CS

Corticosteroids

CT

Computed tomography

CYC

Cyclophosphamide

EF

Eosinophilic fasciitis

EMS

Eosinophilia-myalgia syndrome

HES

Idiopathic hypereosinophilic syndrome

HIV

Human immunodeficiency virus

IgM, IgG, IgA

Immunoglobulin M, G, A

IL

Interleukin

IV

Intravenous

IVIG

Intravenous immunoglobulins

MAC

Membrane attack complex

MPO

Myeloperoxidase antibody

MRA

Magnetic resonance angiography

MRI

Magnetic resonance imaging

p-ANCA

Perinuclear antineutrophil cytoplasmic antibody

PDGFRA

Platelet-derived growth factor receptor alpha

PR3

Proteinase 3 antibodies

PUVA

Psoralen plus ultraviolet A

ROM

Range of motion

sIgMD

Selective Immunoglobulin M Deficiency

TGF β

Transforming growth factor-beta

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Copyright information

© Hospital for Special Surgery 2007

Authors and Affiliations

  • Virginia Florina Haiduc
    • 1
  • Doruk Erkan
    • 1
    • 5
  • Kyriakos Kirou
    • 1
  • Sherri Birchansky
    • 2
  • Josephine Park
    • 3
  • Moris J. Danon
    • 4
  1. 1.Division of RheumatologyHospital for Special SurgeryNew YorkUSA
  2. 2.Department of Radiology and ImagingHospital for Special SurgeryNew YorkUSA
  3. 3.Joint Mobility Center, Department of RehabilitationHospital for Special SurgeryNew YorkUSA
  4. 4.Department of NeurologyHospital for Special SurgeryNew YorkUSA
  5. 5.Barbara Volcker CenterHospital for Special SurgeryNew YorkUSA

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