Abstract
Pseudomyxoma peritonei (PMP) is a rare clinical condition characterized by copious amounts of mucinous ascites and mucinous peritoneal implants. The incidence of PMP is approximately two in 10,000 laparotomies, and about 75% of patients are female with an average age of 53 years. The appendix and ovary comprise the most common sites of origin, and improving immunohistochemical techniques help to identify the origin of the disease. Histologically, three main diagnostic categories are described: the benign form of disseminated peritoneal adenomucinosis (DPAM), the malignant form of peritoneal mucinous carcinomatosis (PMCA), and an intermediate form with features between DPAM and PMCA. Optimal surgical debulking, including peritoneal stripping procedures and appendectomy in combination with intra-/postoperative intraperitoneal chemotherapy, is regarded as the standard treatment.
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Hasenburg, A., Watermann, D.O., Orlowska-Volk, M. et al. Pseudomyxoma peritonei. Eur Clinics Obstet Gynecol 1, 19–23 (2005). https://doi.org/10.1007/s11296-004-0003-0
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DOI: https://doi.org/10.1007/s11296-004-0003-0