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Life-threatening Gross Hematuria due to Genitourinary Manifestation of Klippel–Trenaunay Syndrome

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Abstract

The Klippel–Trenaunay Syndrome (KTS) is defined as a triad of cutaneous capillary malformations, venous varicosities, bone and soft tissue hemi-hypertrophy. The urinary tract is involved in up to 10%. We report the clinical presentation and surgical management of a 9-year-old boy with extensive lympho-venous malformations of the bladder which led to massive recurrent gross hematuria.

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Authors and Affiliations

  1. Department of Urology, Julius-Maximilians-University Medical School, Würzburg, Germany

    Peter Rubenwolf, Alexander Roosen, Elmar W. Gerharz & Hubertus Riedmiller

  2. Department of Pediatrics, Julius-Maximilians-University Medical School, Würzburg, Germany

    Antje Kirchhoff-Moradpour

  3. Institute of Radiology, Julius-Maximilians-University Medical School, Würzburg, Germany

    Kassa Darge

  4. Department of Urology, Julius-Maximilians-University Medical School, Oberduerrbacher Strasse 6, 97080, Wuerzburg, Germany

    Peter Rubenwolf

Authors
  1. Peter Rubenwolf
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  2. Alexander Roosen
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  3. Elmar W. Gerharz
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  4. Antje Kirchhoff-Moradpour
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  5. Kassa Darge
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  6. Hubertus Riedmiller
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Corresponding author

Correspondence to Peter Rubenwolf.

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Rubenwolf, P., Roosen, A., Gerharz, E.W. et al. Life-threatening Gross Hematuria due to Genitourinary Manifestation of Klippel–Trenaunay Syndrome. Int Urol Nephrol 38, 137–140 (2006). https://doi.org/10.1007/s11255-005-3154-0

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  • DOI: https://doi.org/10.1007/s11255-005-3154-0

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