Journal of Neuro-Oncology

, Volume 139, Issue 3, pp 777–778 | Cite as

A unique presentation of an adolescent with disseminated atypical choroid plexus papilloma

  • R. N. Rivière
  • D. L. Johnston
  • E. Story
Letter to the Editor

To the Editor,

We report the case of a 15-year-old male who presented with a 2-month history of sudden right-sided hearing loss. His past medical history was significant for chronic otitis media, with bilateral myringotomy and tympanoplasty at 13-years-of-age to correct a mild conductive hearing loss. His family history was significant for hearing loss and vertigo in his father as a teenager, a pituitary tumor and basal cell carcinoma in his maternal grandmother, and renal cancer in his paternal grandmother.

The patient was initially followed by Otolaryngology who treated him with prednisone for profound right-sided sensorineural hearing loss that was thought to be secondary to a viral infection. Approximately 2 months after his initial presentation, he progressed to profound bilateral sensorineural hearing loss and developed ear pain, dizziness, headaches and vomiting. A CT scan of the temporal bones at this time was unremarkable. An MRI of the head and spine revealed multifocal...



This study was not funded.

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards. This study does not contain any studies with animals performed by any of the authors.

Informed consent

Consent to publish the case study was obtained by the patient and his parents.


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    Talacchi A, De Micheli E, Lombardo C et al (1999) Choroid plexus papilloma of the cerebellopontine angle: a twelve patient series. Surg Neurol 51:621–629CrossRefPubMedGoogle Scholar
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    Pencalet P, Sainte-Rose C, Lellouch-Tubiana A et al (1998) Papillomas and carcinomas of the choroid plexus in children. J Neurosurg 88:521–528CrossRefPubMedGoogle Scholar

Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Faculty of MedicineUniversity of OttawaOttawaCanada
  2. 2.Division of Pediatric Hematology/OncologyChildren’s Hospital of Eastern Ontario (CHEO)OttawaCanada

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