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Dumbbell-shaped peripheral primitive neuroectodermal tumor of the spine—case report and review of the literature

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Abstract

Primary spinal peripheral primitive neuroectodermal tumors (pPNETs) are extremely rare. Here, we present a case study of a 29-year-old male with a dumbbell-shaped pPNET at the T9-10 spine level, including details of his examination, surgical procedures applied, histological and genetic findings, and his subsequent treatment. We discuss the clinical course, the pathology and treatment for this disease, the surgical approach to thoracic dumbbell tumors and we review the literature. To our knowledge, this is the first report of a case of a dumbbell-shaped intradural and spinal peripheral PNET.

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Acknowledgments

This project was supported, in part, by grants from the Ministry of School and Education (MSM 6198959216 and LC07017) and the Ministry of Industry and Trade of the Czech Republic (MPO 1H-PK/45).

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Authors and Affiliations

  1. University Hospital Olomouc, Olomouc, Czech Republic

    Lumír Hrabálek, Ondrej Kalita, Hana Svebisova, Jiri Ehrmann Jr., Marian Hajduch, Radek Trojanec & Miroslav Kala

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  1. Lumír Hrabálek
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Correspondence to Lumír Hrabálek.

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Hrabálek, L., Kalita, O., Svebisova, H. et al. Dumbbell-shaped peripheral primitive neuroectodermal tumor of the spine—case report and review of the literature. J Neurooncol 92, 211–217 (2009). https://doi.org/10.1007/s11060-008-9744-9

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