|
Characteristic
|
Children
|
Adolescents
|
Adults
|
|---|
|
2–11 years
|
12–15 years
|
16–64 years
|
|---|
|
N = 18
|
N = 5
|
N = 28
|
|---|
|
Gender, n (%)
|
|
Female
|
5 (27.8)
|
0 (0)
|
11 (39.3)
|
|
Male
|
13 (72.2)
|
5 (100)
|
17 (60.7)
|
|
Age (years)
|
|
Mean (SD)
|
7.2 (2.5)
|
14.0 (1.0)
|
34.1 (12.7)
|
|
Median (Range)
|
7.5 (3–11)
|
14.0 (13–15)
|
32.5 (16–60)
|
|
Weight (kg)
|
|
Mean (SD)
|
25.9 (11.06)
|
57.1 (15.84)
|
69.2 (13.34)
|
|
Median (Range)
|
22.0 (13–56)
|
53.3 (36–77)
|
70.2 (41–96)
|
|
BMI (kg/m2)
|
|
Mean (SD)
|
16.4 (2.88)
|
20.6 (2.29)
|
23.3 (3.96)
|
|
Median (Range)
|
15.3 (12–24)
|
20.1 (18–23)
|
23.0 (16–32)
|
|
Primary disease
|
|
CVID, n (%)
|
7 (38.9)
|
0 (0)
|
23 (82.1)
|
|
XLA, n (%)
|
10 (55.6)
|
5 (100)
|
5 (17.9)
|
|
ARAG, n (%)
|
1 (5.6)
|
0 (0)
|
0 (0)
|
-
AT all treated (23 pediatric patients), N number of patients in age group, SD standard deviation, CVID common variable immunodeficiency, XLA X-linked agammaglobulinemia, ARAG autosomal recessive agammaglobulinemia